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Myocardial function, heart failure and arrhythmia in Marfan syndrome : a systematic literature review

(2020) DIAGNOSTICS. 10(10).
Author
Organization
Abstract
Marfan syndrome (MFS) is a heritable systemic connective tissue disease with important cardiovascular involvement, including aortic root dilatation and mitral valve prolapse. Life expectancy in patients with MFS is mainly determined by cardiovascular complications, among which aortic dissection or rupture are most dreaded. In recent years, heart failure and ventricular arrhythmia have drawn attention as extra-aortic cardiovascular manifestations and as additional reported causes of death. Imaging studies have provided data supporting a primary myocardial impairment in the absence of valvular disease or cardiovascular surgery, while studies using ambulatory ECG have demonstrated an increased susceptibility to ventricular arrhythmia. In this paper, current literature was reviewed in order to provide insights in characteristics, pathophysiology and evolution of myocardial function, heart failure and ventricular arrhythmia in MFS.
Keywords
Marfan syndrome, heart failure, myocardial, ventricular arrhythmia, LEFT-VENTRICULAR FUNCTION, ATRIOVENTRICULAR PLANE DISPLACEMENT, AORTIC ROOT REPLACEMENT, SUDDEN CARDIAC DEATH, EXTRACELLULAR-MATRIX, LIFE EXPECTANCY, GHENT NOSOLOGY, YOUNG-ADULTS, STRAIN-RATE, FOLLOW-UP

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MLA
Demolder, Anthony, et al. “Myocardial Function, Heart Failure and Arrhythmia in Marfan Syndrome : A Systematic Literature Review.” DIAGNOSTICS, vol. 10, no. 10, 2020, doi:10.3390/diagnostics10100751.
APA
Demolder, A., von Kodolitsch, Y., Muiño Mosquera, L., & De Backer, J. (2020). Myocardial function, heart failure and arrhythmia in Marfan syndrome : a systematic literature review. DIAGNOSTICS, 10(10). https://doi.org/10.3390/diagnostics10100751
Chicago author-date
Demolder, Anthony, Yskert von Kodolitsch, Laura Muiño Mosquera, and Julie De Backer. 2020. “Myocardial Function, Heart Failure and Arrhythmia in Marfan Syndrome : A Systematic Literature Review.” DIAGNOSTICS 10 (10). https://doi.org/10.3390/diagnostics10100751.
Chicago author-date (all authors)
Demolder, Anthony, Yskert von Kodolitsch, Laura Muiño Mosquera, and Julie De Backer. 2020. “Myocardial Function, Heart Failure and Arrhythmia in Marfan Syndrome : A Systematic Literature Review.” DIAGNOSTICS 10 (10). doi:10.3390/diagnostics10100751.
Vancouver
1.
Demolder A, von Kodolitsch Y, Muiño Mosquera L, De Backer J. Myocardial function, heart failure and arrhythmia in Marfan syndrome : a systematic literature review. DIAGNOSTICS. 2020;10(10).
IEEE
[1]
A. Demolder, Y. von Kodolitsch, L. Muiño Mosquera, and J. De Backer, “Myocardial function, heart failure and arrhythmia in Marfan syndrome : a systematic literature review,” DIAGNOSTICS, vol. 10, no. 10, 2020.
@article{8676376,
  abstract     = {Marfan syndrome (MFS) is a heritable systemic connective tissue disease with important cardiovascular involvement, including aortic root dilatation and mitral valve prolapse. Life expectancy in patients with MFS is mainly determined by cardiovascular complications, among which aortic dissection or rupture are most dreaded. In recent years, heart failure and ventricular arrhythmia have drawn attention as extra-aortic cardiovascular manifestations and as additional reported causes of death. Imaging studies have provided data supporting a primary myocardial impairment in the absence of valvular disease or cardiovascular surgery, while studies using ambulatory ECG have demonstrated an increased susceptibility to ventricular arrhythmia. In this paper, current literature was reviewed in order to provide insights in characteristics, pathophysiology and evolution of myocardial function, heart failure and ventricular arrhythmia in MFS.},
  articleno    = {751},
  author       = {Demolder, Anthony and von Kodolitsch, Yskert and Muiño Mosquera, Laura and De Backer, Julie},
  issn         = {2075-4418},
  journal      = {DIAGNOSTICS},
  keywords     = {Marfan syndrome,heart failure,myocardial,ventricular arrhythmia,LEFT-VENTRICULAR FUNCTION,ATRIOVENTRICULAR PLANE DISPLACEMENT,AORTIC ROOT REPLACEMENT,SUDDEN CARDIAC DEATH,EXTRACELLULAR-MATRIX,LIFE EXPECTANCY,GHENT NOSOLOGY,YOUNG-ADULTS,STRAIN-RATE,FOLLOW-UP},
  language     = {eng},
  number       = {10},
  pages        = {21},
  title        = {Myocardial function, heart failure and arrhythmia in Marfan syndrome : a systematic literature review},
  url          = {http://dx.doi.org/10.3390/diagnostics10100751},
  volume       = {10},
  year         = {2020},
}

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