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Hippocampal atrophy and developmental regression as first sign of linear scleroderma "en coup de sabre"

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Abstract
An 8-year-old girl with linear scleroderma "en coup de sabre" is reported who, at preschool age, presented with intractable simple partial seizures more than 1 year before skin lesions were first noticed. MRI revealed hippocampal atrophy, controlaterally to the seizures and ipsilaterally to the skin lesions. in the following months, a mental and motor regression was noticed. Cerebral CT scan showed multiple foci of calcifications in the affected hemisphere. In previously reported patients the skin lesions preceded the neurological signs. To the best of our knowledge, hippocampal atrophy was not earlier reported as presenting symptom of linear scleroderma. Linear scleroderma should be included in the differential diagnosis in patients with unilateral hippocampal. atrophy even when the typical skin lesions are not present. (C) 2008 European Paediatric Neurology Society. Published by Elsevier Ltd. All rights reserved.
Keywords
Linear scleroderma, Hippocampal atrophy, Developmental regression, Children

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Chicago
VERHELST, HELENE, Hilde Beele, Rik Joos, Benedicte Vanneuville, and Rudy Van Coster. 2008. “Hippocampal Atrophy and Developmental Regression as First Sign of Linear Scleroderma ‘En Coup De Sabre’.” European Journal of Paediatric Neurology 12 (6): 508–511.
APA
VERHELST, H., Beele, H., Joos, R., Vanneuville, B., & Van Coster, R. (2008). Hippocampal atrophy and developmental regression as first sign of linear scleroderma “en coup de sabre.” EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY, 12(6), 508–511.
Vancouver
1.
VERHELST H, Beele H, Joos R, Vanneuville B, Van Coster R. Hippocampal atrophy and developmental regression as first sign of linear scleroderma “en coup de sabre.”EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY. THE BOULEVARD, LANGFORD LANE, KIDLINGTON, OXFORD OX5 1GB, OXON, ENGLAND: ELSEVIER SCI LTD; 2008;12(6):508–11.
MLA
VERHELST, HELENE, Hilde Beele, Rik Joos, et al. “Hippocampal Atrophy and Developmental Regression as First Sign of Linear Scleroderma ‘En Coup De Sabre’.” EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY 12.6 (2008): 508–511. Print.
@article{527196,
  abstract     = {An 8-year-old girl with linear scleroderma {\textacutedbl}en coup de sabre{\textacutedbl} is reported who, at preschool age, presented with intractable simple partial seizures more than 1 year before skin lesions were first noticed. MRI revealed hippocampal atrophy, controlaterally to the seizures and ipsilaterally to the skin lesions. in the following months, a mental and motor regression was noticed. Cerebral CT scan showed multiple foci of calcifications in the affected hemisphere. In previously reported patients the skin lesions preceded the neurological signs. To the best of our knowledge, hippocampal atrophy was not earlier reported as presenting symptom of linear scleroderma. Linear scleroderma should be included in the differential diagnosis in patients with unilateral hippocampal. atrophy even when the typical skin lesions are not present. (C) 2008 European Paediatric Neurology Society. Published by Elsevier Ltd. All rights reserved.},
  author       = {VERHELST, HELENE and Beele, Hilde and Joos, Rik and Vanneuville, Benedicte and Van Coster, Rudy},
  issn         = {1090-3798},
  journal      = {EUROPEAN JOURNAL OF PAEDIATRIC NEUROLOGY},
  keyword      = {Linear scleroderma,Hippocampal atrophy,Developmental regression,Children},
  language     = {eng},
  number       = {6},
  pages        = {508--511},
  publisher    = {ELSEVIER SCI LTD},
  title        = {Hippocampal atrophy and developmental regression as first sign of linear scleroderma {\textacutedbl}en coup de sabre{\textacutedbl}},
  url          = {http://dx.doi.org/10.1016/j.ejpn.2007.12.001},
  volume       = {12},
  year         = {2008},
}

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