Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome
- Author
- SVEN DEKEYZER (UGent) , BRECHT HOUTHOOFD (UGent) , ALEXANDRA DE POTTER (UGent) , Mieke Van Bockstal (UGent) , Peter Smeets (UGent) and Dirk Vogelaers (UGent)
- Organization
- Abstract
- Klippel-Trénaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trénaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy.
- Keywords
- Angioma, Spleen Diseases
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Citation
Please use this url to cite or link to this publication: http://hdl.handle.net/1854/LU-4412877
- MLA
- DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, et al. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” JBR-BTR 96.6 (2013): 357–359. Print.
- APA
- DEKEYZER, SVEN, HOUTHOOFD, B., DE POTTER, A., Van Bockstal, M., Smeets, P., & Vogelaers, D. (2013). Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome. JBR-BTR, 96(6), 357–359.
- Chicago author-date
- DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, Mieke Van Bockstal, Peter Smeets, and Dirk Vogelaers. 2013. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” Jbr-btr 96 (6): 357–359.
- Chicago author-date (all authors)
- DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, Mieke Van Bockstal, Peter Smeets, and Dirk Vogelaers. 2013. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” Jbr-btr 96 (6): 357–359.
- Vancouver
- 1.DEKEYZER S, HOUTHOOFD B, DE POTTER A, Van Bockstal M, Smeets P, Vogelaers D. Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome. JBR-BTR. 2013;96(6):357–9.
- IEEE
- [1]S. DEKEYZER, B. HOUTHOOFD, A. DE POTTER, M. Van Bockstal, P. Smeets, and D. Vogelaers, “Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome,” JBR-BTR, vol. 96, no. 6, pp. 357–359, 2013.
@article{4412877,
abstract = {Klippel-Trénaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trénaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy.},
author = {DEKEYZER, SVEN and HOUTHOOFD, BRECHT and DE POTTER, ALEXANDRA and Van Bockstal, Mieke and Smeets, Peter and Vogelaers, Dirk},
issn = {1780-2393},
journal = {JBR-BTR},
keywords = {Angioma,Spleen Diseases},
language = {eng},
number = {6},
pages = {357--359},
title = {Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome},
url = {http://www.rbrs.org/template.php?sect=4&subs=4&id=75},
volume = {96},
year = {2013},
}