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Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome

SVEN DEKEYZER (UGent) , BRECHT HOUTHOOFD (UGent) , ALEXANDRA DE POTTER (UGent) , Mieke Van Bockstal (UGent) , Peter Smeets (UGent) and Dirk Vogelaers (UGent)
(2013) JBR-BTR. 96(6). p.357-359
Author
Organization
Abstract
Klippel-Trénaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trénaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy.
Keywords
Angioma, Spleen Diseases

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MLA
DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, et al. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” JBR-BTR 96.6 (2013): 357–359. Print.
APA
DEKEYZER, SVEN, HOUTHOOFD, B., DE POTTER, A., Van Bockstal, M., Smeets, P., & Vogelaers, D. (2013). Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome. JBR-BTR, 96(6), 357–359.
Chicago author-date
DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, Mieke Van Bockstal, Peter Smeets, and Dirk Vogelaers. 2013. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” Jbr-btr 96 (6): 357–359.
Chicago author-date (all authors)
DEKEYZER, SVEN, BRECHT HOUTHOOFD, ALEXANDRA DE POTTER, Mieke Van Bockstal, Peter Smeets, and Dirk Vogelaers. 2013. “Hemangiomatosis of the Spleen in a Patient with Klippel-Trénaunay Syndrome.” Jbr-btr 96 (6): 357–359.
Vancouver
1.
DEKEYZER S, HOUTHOOFD B, DE POTTER A, Van Bockstal M, Smeets P, Vogelaers D. Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome. JBR-BTR. 2013;96(6):357–9.
IEEE
[1]
S. DEKEYZER, B. HOUTHOOFD, A. DE POTTER, M. Van Bockstal, P. Smeets, and D. Vogelaers, “Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome,” JBR-BTR, vol. 96, no. 6, pp. 357–359, 2013.
@article{4412877,
  abstract     = {Klippel-Trénaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trénaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy.},
  author       = {DEKEYZER, SVEN and HOUTHOOFD, BRECHT and DE POTTER, ALEXANDRA and Van Bockstal, Mieke and Smeets, Peter and Vogelaers, Dirk},
  issn         = {1780-2393},
  journal      = {JBR-BTR},
  keywords     = {Angioma,Spleen Diseases},
  language     = {eng},
  number       = {6},
  pages        = {357--359},
  title        = {Hemangiomatosis of the spleen in a patient with Klippel-Trénaunay syndrome},
  url          = {http://www.rbrs.org/template.php?sect=4&subs=4&id=75},
  volume       = {96},
  year         = {2013},
}

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