Further delineation of the DFNA5 phenotype: Results of speech recognition tests
- Author
- Els De Leenheer (UGent) , DA VAN ZUIJLEN, Lut Van Laer (UGent) , G VAN CAMP, P HUYGEN, EH HUIZING and C CREMERS
- Organization
- Abstract
- Speech recognition scores were analyzed in 34 carriers of a DFNA5 mutation. Cross-sectional linear regression analysis (last visit, maximum recognition score in %Correct on age or PTA(1,2,4 kHz)) established onset age (score 90%) at 16 years and onset PTA(1,2,4 kHz) level (score 90%) at 41 dB hearing level. The deterioration rate was 0.7%/y in the plot of maximum score against age, whereas the deterioration gradient was 0.4%/dB in the plot of maximum score against PTA(1,2.4 kHz). Given the previously demonstrated rapid progression of hearing impairment, speech recognition was relatively good: at age 70, the score was still >50%.
Citation
Please use this url to cite or link to this publication: http://hdl.handle.net/1854/LU-165565
- MLA
- De Leenheer, Els, et al. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, vol. 111, no. 7, 2002, pp. 639–41.
- APA
- De Leenheer, E., VAN ZUIJLEN, D., Van Laer, L., VAN CAMP, G., HUYGEN, P., HUIZING, E., & CREMERS, C. (2002). Further delineation of the DFNA5 phenotype: Results of speech recognition tests. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 111(7), 639–641.
- Chicago author-date
- De Leenheer, Els, DA VAN ZUIJLEN, Lut Van Laer, G VAN CAMP, P HUYGEN, EH HUIZING, and C CREMERS. 2002. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY 111 (7): 639–41.
- Chicago author-date (all authors)
- De Leenheer, Els, DA VAN ZUIJLEN, Lut Van Laer, G VAN CAMP, P HUYGEN, EH HUIZING, and C CREMERS. 2002. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY 111 (7): 639–641.
- Vancouver
- 1.De Leenheer E, VAN ZUIJLEN D, Van Laer L, VAN CAMP G, HUYGEN P, HUIZING E, et al. Further delineation of the DFNA5 phenotype: Results of speech recognition tests. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY. 2002;111(7):639–41.
- IEEE
- [1]E. De Leenheer et al., “Further delineation of the DFNA5 phenotype: Results of speech recognition tests,” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, vol. 111, no. 7, pp. 639–641, 2002.
@article{165565,
abstract = {{Speech recognition scores were analyzed in 34 carriers of a DFNA5 mutation. Cross-sectional linear regression analysis (last visit, maximum recognition score in %Correct on age or PTA(1,2,4 kHz)) established onset age (score 90%) at 16 years and onset PTA(1,2,4 kHz) level (score 90%) at 41 dB hearing level. The deterioration rate was 0.7%/y in the plot of maximum score against age, whereas the deterioration gradient was 0.4%/dB in the plot of maximum score against PTA(1,2.4 kHz). Given the previously demonstrated rapid progression of hearing impairment, speech recognition was relatively good: at age 70, the score was still >50%.}},
author = {{De Leenheer, Els and VAN ZUIJLEN, DA and Van Laer, Lut and VAN CAMP, G and HUYGEN, P and HUIZING, EH and CREMERS, C}},
issn = {{0003-4894}},
journal = {{ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY}},
language = {{eng}},
number = {{7}},
pages = {{639--641}},
title = {{Further delineation of the DFNA5 phenotype: Results of speech recognition tests}},
volume = {{111}},
year = {{2002}},
}