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Further delineation of the DFNA5 phenotype: Results of speech recognition tests

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Abstract
Speech recognition scores were analyzed in 34 carriers of a DFNA5 mutation. Cross-sectional linear regression analysis (last visit, maximum recognition score in %Correct on age or PTA(1,2,4 kHz)) established onset age (score 90%) at 16 years and onset PTA(1,2,4 kHz) level (score 90%) at 41 dB hearing level. The deterioration rate was 0.7%/y in the plot of maximum score against age, whereas the deterioration gradient was 0.4%/dB in the plot of maximum score against PTA(1,2.4 kHz). Given the previously demonstrated rapid progression of hearing impairment, speech recognition was relatively good: at age 70, the score was still >50%.

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MLA
De Leenheer, Els, et al. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, vol. 111, no. 7, 2002, pp. 639–41.
APA
De Leenheer, E., VAN ZUIJLEN, D., Van Laer, L., VAN CAMP, G., HUYGEN, P., HUIZING, E., & CREMERS, C. (2002). Further delineation of the DFNA5 phenotype: Results of speech recognition tests. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 111(7), 639–641.
Chicago author-date
De Leenheer, Els, DA VAN ZUIJLEN, Lut Van Laer, G VAN CAMP, P HUYGEN, EH HUIZING, and C CREMERS. 2002. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY 111 (7): 639–41.
Chicago author-date (all authors)
De Leenheer, Els, DA VAN ZUIJLEN, Lut Van Laer, G VAN CAMP, P HUYGEN, EH HUIZING, and C CREMERS. 2002. “Further Delineation of the DFNA5 Phenotype: Results of Speech Recognition Tests.” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY 111 (7): 639–641.
Vancouver
1.
De Leenheer E, VAN ZUIJLEN D, Van Laer L, VAN CAMP G, HUYGEN P, HUIZING E, et al. Further delineation of the DFNA5 phenotype: Results of speech recognition tests. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY. 2002;111(7):639–41.
IEEE
[1]
E. De Leenheer et al., “Further delineation of the DFNA5 phenotype: Results of speech recognition tests,” ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, vol. 111, no. 7, pp. 639–641, 2002.
@article{165565,
  abstract     = {{Speech recognition scores were analyzed in 34 carriers of a DFNA5 mutation. Cross-sectional linear regression analysis (last visit, maximum recognition score in %Correct on age or PTA(1,2,4 kHz)) established onset age (score 90%) at 16 years and onset PTA(1,2,4 kHz) level (score 90%) at 41 dB hearing level. The deterioration rate was 0.7%/y in the plot of maximum score against age, whereas the deterioration gradient was 0.4%/dB in the plot of maximum score against PTA(1,2.4 kHz). Given the previously demonstrated rapid progression of hearing impairment, speech recognition was relatively good: at age 70, the score was still >50%.}},
  author       = {{De Leenheer, Els and VAN ZUIJLEN, DA and Van Laer, Lut and VAN CAMP, G and HUYGEN, P and HUIZING, EH and CREMERS, C}},
  issn         = {{0003-4894}},
  journal      = {{ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY}},
  language     = {{eng}},
  number       = {{7}},
  pages        = {{639--641}},
  title        = {{Further delineation of the DFNA5 phenotype: Results of speech recognition tests}},
  volume       = {{111}},
  year         = {{2002}},
}

Web of Science
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